An Unusual Congenital Anomaly in Fanconi Aplastic Anemia: Congenital Lobar Emphysema
نویسندگان
چکیده
منابع مشابه
An Unusual Congenital Anomaly in Fanconi Aplastic Anemia: Congenital Lobar Emphysema
A 7-year-old girl who presented with epistaxis was examined due to pancytopenia. Her medical history revealed that she had respiratory distress in the neonatal period. She was born to a second-degree consanguineous marriage. Physical examination revealed short stature, microcephaly, microphthalmia, and hypo/ hyperpigmented lesions on the trunk and extremities. She did not have tachypnea, but sh...
متن کاملCongenital Lobar Emphysema
Over the past four years (1360-1364) we have surgically treated seven infants for lobar emphysema. The pathologic lesion in all patients was in upper lobe of the left lung. Respiratory distress and pneumonia are the cardinal symptoms of patients with this abnormality. Diagnosis is confirmed by chest x-ray. The treatment of choice is lobectomy of affected lobe.
متن کاملAn Unusual Presentation of Congenital Lobar Emphysema
Congenital lobar emphysema is an uncommon bronchopulmonary malformation characterized by lobar overinflation and accompanying alveolar septum damage that leads to compression atelectasis of the lung parenchyma and displacement of mediastinal structures, with the resultant ventilation-perfusion mismatch. We present a case of a 33-year-old lady with progressive exertional dyspnea. Chest radiograp...
متن کاملCongenital Lobar Emphysema : a case Report
This case is a bout a neonate with respiratory distress and primary diagnosis of Pneumothorax who had Congenital Lobar Emphysema. This case was the basis to review the topic of Congenital Lobar Emphysema (CLE) and the corresponding literature, considering that this is an uncommon disease and although congenital lobar emphysema is rare, clinical awareness of this condition is important for early...
متن کاملCongenital Lobar Emphysema
Regional obstructive emphysema is not uncommon and is due in most cases to obstruction of a bronchus by secretions, tumour, foreign body or glands. Cohen (1943) described such a condition in association with a bronchial carcinoma and Spivek (1936) mentioned a similar picture in connexion with tuberculous glands. In such cases, however, the obstruction is usually progressive and leads finally to...
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ژورنال
عنوان ژورنال: Turkish Journal of Hematology
سال: 2016
ISSN: 1300-7777
DOI: 10.4274/tjh.2015.0384